Proteolysis of mutant huntingtin produces an exon 1 fragment that accumulates as an aggregated protein in neuronal nuclei in Huntington disease
Journal of Biological Chemistry (2010) - Comments
pubmed: 20086007  doi: 10.1074/jbc.m109.075028  issn: 0021-9258  issn: 1083-351x 

Christian Landles, Kirupa Sathasivam, Andreas Weiss, Ben Woodman, Hilary Moffitt, Steve Finkbeiner, Banghua Sun, Juliette Gafni, Lisa M. Ellerby, Yvon Trottier, William G. Richards, Alex Osmand, Paolo Paganetti, Gillian P. Bates